ANSWER: Name Syndrome – Test Question

The correct answer is A. Peg or conical teeth

Correct Answer Explanation

Peg/conical teeth are not part of the Carney complex. This is found in incontinentia pigmenti and anhidrotic ectodermal dysplasia.

Incorrect Answer Explanation

The remaining skin findings are part of this complex sometimes known as NAME syndrome. It consists of multiple, diffuse mucocutaneous lentigines, cardiac and subcutaneous myxomas, and endocrine abnormalities may be present. Other findings include testicular tumors, thyroid disease, primary pigmented nodular adrenocortical disease, psammomatous melanotic schwannomas, and hormone-secreting pituitary adenomas.


Liu Q, Tong D, Liu G, Yi Y, Zhang D, Zhang J, Zhang Y, Huang Z, Li Y, Chen R, Guan Y, Yi X, Jiang J. Carney complex with PRKAR1A gene mutation: A case report and literature review. Medicine (Baltimore). 2017 Dec;96(50):e8999. PMID: 29390296