Malignant proliferating trichilemmal tumors are rare adnexal neoplasms that most commonly occur on the scalp in elderly women. These tumors are associated with recurrence and even nodal or distant metastatic spread. Here, JDD authors describe a 38-year-old patient who presented with a scalp nodule that was diagnosed as a high-grade malignant proliferating trichilemmal tumor.
Although malignant proliferating trichilemmal tumors most commonly occur in the 8th to 9th decade of life, we present a case of a high-grade tumor occurring in a 38-year-old woman. Given the risk of recurrence and metastasis in such lesions, appropriate identification of this rare neoplasm in younger patients will hasten treatment and improve prognosis.
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Allison Weiffenbach MD, Kimberly L. Katz MD, Katherine A. Rupley MD, Adam J. Carter MD, Alice Gottlieb MD PhD, Kenneth Shulman MD, (2018). Rapidly Enlarging Malignant Proliferating Trichilemmal Tumor in a Young Female. Journal of Drugs in Dermatology, 17(12), 1325-1327.
Content and images used with permission from the Journal of Drugs in Dermatology.
Adapted from original article for length and style.
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